Epithelioid schwannoma or ossifying fibromyxoid tumour?

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There is a risk of confusing epithelioid schwannoma and ossifying fibromyxoid tumors due to their similar morphological and immunohistochemical features. Epithelioid schwannoma can be described as a benign nerve sheath tumour of peripheral nerves. Ossifying fibromyxoid tumour is considered to be a intermediate malignant soft tissue tumour with the potential for recurrence and metastasis. Because the prognosis of these two tumoral entities are different from each other differential diagnosis is important. In this article, our purpose is to present a case, on what we initially considered to be epithelioid schwannoma. However, we later observed, based on the data in the literature,
that the tumour appeared to be an ossifying fibromyxoid tumour.


Epithelioid Fibromyxoid; ossifying; schwannoma; tumour

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DOI: http://dx.doi.org/10.5835/jecm.omu.30.02.023


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